Pulmonary Sequestration

What is a pulmonary sequestration?

A pulmonary sequestration is a cystic mass of abnormal lung tissue that develops during pregnancy and doesn’t function like normal lung tissue. Pulmonary sequestrations can appear next to the lung or embedded within part of the lung. 

Congenital pulmonary airway malformation (CPAM), formerly known as congenital cystic adenomatoid malformation (CCAM), is a similar type of lung mass. The main difference between a pulmonary sequestration and CPAM is the presence of a blood vessel. A pulmonary sequestration develops its own artery that connects directly to the aorta. 

How do I know if my baby has a pulmonary sequestration?

A pulmonary sequestration is a congenital condition, which means it’s present at birth. Your doctor may detect the abnormal mass on a prenatal ultrasound. California Pediatric Surgical Group carefully evaluates the ultrasound images and reviews possible diagnoses during your prenatal consultation.

California Pediatric Surgical Group answers any questions you may have and helps you prepare for what to expect every step of the way. 

How does a pulmonary sequestration affect delivery?

Having any type of lung malformation increases your baby’s risk for complications during and after delivery, so it’s important to be prepared in case something goes wrong. California Pediatric Surgical Group works with the multidisciplinary team at Ventura County Medical Center to provide you and your baby with elite-level care close to home.

How is a pulmonary sequestration diagnosed and treated?

After birth, your California Pediatric Surgical Group surgeon carefully evaluates your baby’s condition. They take diagnostic tests, such as a chest X-ray or ultrasound, to confirm or rule out a pulmonary sequestration. Then, they recommend the best course of treatment.

Though a pulmonary sequestration or CPAM may not be life-threatening, they can lead to long-term problems later in life, including tuberculosis and bronchial cancer. Surgically removing the mass is the most common treatment. 

Depending on the size, type, and severity of the mass, California Pediatric Surgical Group may perform surgery right after birth or they may schedule the surgery for a later time during your baby’s first year. 

If you suspect your baby has a pulmonary sequestration or CPAM, call California Pediatric Surgical Group or book an appointment online today.